Estenosis aortica supravalvular pdf

It is often associated with other cardiovascular anomalies and is one of the characteristic findings of williams syndrome. Links to pubmed are also available for selected references. Estenosis aortica lucile packard childrens hospital stanford. Estenosis aortica trastornos cardiovasculares manual msd. Supravalvular aortic stenosis surgical repair using. Supravalvular aortic stenosis genetic and rare diseases. Department of surgery supravalvular aortic stenosis. Supravalvular aortic stenosis is a congenital obstructive narrowing of the aorta just above the aortic valve and is second most common type of aortic stenosis. Supravalvular aortic stenosis svas is a type of heart defect that develops before birth. Jul 20, 2017 the aortic root in supravalvular aortic stenosis. However, the available data have been limited to small family groups which do. Estenosis aortica valvular, subvalvular y supravalvular.

The condition is described as supravalvular because the section of the aorta that is narrowed is located just above the valve. Estenosis aortica valvular, subvalvular y supravalvular dra. It is characterized by a narrowing stenosis of the section of the aorta just above the valve that connects the aorta to the heart aortic valve. Cove point contains comprehensive information on all congenital heart defects, including atrial septal defect asd, ventricular septal defect vsd, hypoplastic left heart syndrome hlhs, and tetralogy of fallot tof. It accounts for less than 7% of all fixed forms of congenital lvot obstructive lesions. Estenosis supravalvular aortica linkedin slideshare. Estenosis aortica cardiologia pediatrica area del corazon. The surgical treatment of supravalvular aortic stenosis. Issues and outcomes in the management of supravalvar aortic stenosis. Elastin, supravalvular aortic stenosis, peripheral pulmonary artery stenosis, eln excluded diseases supravalvular aortic stenosis svas should be differentiated from. This defect is a narrowing stenosis of the large blood vessel that carries blood from the heart to the rest of the body the aorta.